A Clinical Experience of Neurofibromatosis Involving Periorbital Region

Korean Journal of Head & Neck Oncology 1997;13(1):86-89.
Published online May 30, 1997.

Dae Hwan Park;Tae Mo Kim;Dong Gil Han;Ki Young Ahn

안와부위에 발생한 신경섬유종증의 임상적 치험례

박대환;김태모;한동길;안기영

Abstract

Neurofibromatosis, now termed neurofibromatosis type I, is known as a congenital and familial disease presenting abnormalities of the skin, nervous system, bones, and soft tissue. We experienced a case of extremely large neurofibromatosis which developed on the orbital and temporal region of a 24-year-old man. The tumor was widely excised including normal skin margin, outer table of cranium, a part of zygoma and maxilla. Bony defect was reconstructed by rib bone graft and secondary cosmetic correction of blepharoptosis was performed using supratarsal fixation in postoperative 6 months.

Key Words: Neurofibromatosis, Orbit