A Case of Embryonal Rhabdomyosarcoma at Left Parotid Gland in 8-Month-Old Infant

Korean Journal of Head & Neck Oncology 2014;30(2):119-122.
Published online November 30, 2014.

Minhyuk Cho;Yeon Soo Kim;YooSeob Shin;Chul-Ho Kim

8개월 영아의 좌측 이하선 부위에서 발생한 배아형 횡문근육종 1예

조민혁;김연수;신유섭;김철호

Abstract

Rhabdomyosarcoma is the most common sarcoma in children less than 15 years of age. Two major histological subtypes are embryonal and alveolar. Embryonal rhabdomyosarcoma is diagnosed by immunopathology and treat-ments require coordinated management plans that include surgery, chemotherapy, and usually radiotherapy. 8-month-old male infant visited with swelling in left parotid area. Computed tomography scan showed a hetero- geneous mass in the left parotid area and the result of fine-needle aspiration cytology was suspicious malignancy. Left total parotidectomy was performed and CSF leakage was noted and repaired. Confirmed by positive reactions to desmin and myogenin, the diagnosis was embryonal rhabdomyosarcoma. On postoperative brain MRI, extension along the meninges was noted and for treatment, chemotherapy and gamma knife radiosurgery were done. Five years after initial surgical resection(3 years and 10 months after completion of chemotherapy and gamma knife radiosurgery), the child did not show any evidence of local recurrence or distant metastasis.

Key Words: Embryonal rhabdomyosarcoma, Parotid gland, Children, Pediatric gamma knife radiosurgery